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Dernières publications
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Francesco Galli, Laricia Bragg, Maira Rossi, Daisy Proietti, Laura Perani, et al.. Cell-mediated exon skipping normalizes dystrophin expression and muscle function in a new mouse model of Duchenne Muscular Dystrophy. EMBO Molecular Medicine, 2024, 16 (4), pp.927 - 944. ⟨10.1038/s44321-024-00031-3⟩. ⟨hal-04603972⟩
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Ekaterina Kiseleva, Olesya Serbina, Anna Karpukhina, Vincent Mouly, Yegor S Vassetzky. Interaction between mesenchymal stem cells and myoblasts in the context of facioscapulohumeral muscular dystrophy contributes to the disease phenotype. Journal of Cellular Physiology, 2022, 237 (8), pp.3328-3337. ⟨10.1002/jcp.30789⟩. ⟨hal-03796151⟩
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Muhammad Haseeb Iqbal, Jeanne Rosine Faratiana, Emeline Pradel, Varvara Gribova, Kamel Mamchaoui, et al.. Brush-Induced Orientation of Collagen Fibers in Layer-by-Layer Nanofilms: A Simple Method for the Development of Human Muscle Fibers. ACS Nano, In press, ⟨10.1021/acsnano.2c06329⟩. ⟨hal-03832239⟩
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Elena Marchesi, Matteo Bovolenta, Lorenzo Preti, Massimo L Capobianco, Kamel Mamchaoui, et al.. Synthesis and Exon-Skipping Properties of a 3′-Ursodeoxycholic Acid-Conjugated Oligonucleotide Targeting DMD Pre-mRNA: Pre-Synthetic versus Post-Synthetic Approach. Molecules, 2021, 26 (24), pp.7662. ⟨10.3390/molecules26247662⟩. ⟨hal-03510261⟩
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Manuel Schmidt, Anja Weidemann, Christine Poser, Anne Bigot, Julia von Maltzahn. Stimulation of Non-canonical NF-κB Through Lymphotoxin-β-Receptor Impairs Myogenic Differentiation and Regeneration of Skeletal Muscle. Frontiers in Cell and Developmental Biology, 2021, 9, ⟨10.3389/fcell.2021.721543⟩. ⟨hal-03405959⟩
Chiffres clés
Open Access
87 %
Mots clés
Expanded repeats
3D co-culture
Duchenne Muscular Dystrophy
Computer software
Fibrosis
CXCL12
Dystrophin
LRP4
Immortalized dystrophic canine myoblast
Acetylcholine receptor subunit epsilon
Exon Skipping
CXCR4
Lymphotoxin-β-receptor
Adeno-associated viral vector
Myogenesis
Human
Machine learning
CTG⋅CAGn repeat
Alternative splicing
FoxO
Dominant centronuclear myopathy
DNM2
DiPRO1
Adhesion
Canine X-linked muscular dystrophy in Japan CXMD J
BMD
Glucocorticoid-induced muscle atrophy
Autophagosome
FSHD
Endocytosis
ICU-acquired weakness
LTβR
HDMD/Dmd-null mice
Cell Therapy
MSCs
Emerin
DsDNA break repair
Myotonic dystrophy
Actin
Exon-skipping
Clinical trial candidate screening
Antisense oligonucleotide
Flavonoid
Gene Therapy
Dynamin 2
Fear response
Gel electrophoresis
CFTR correctors
Exon skipping
CDNA synthesis
ITSN1
Atrial cardiac defects
Centronuclear myopathy
Fibroblast
DM1 myoblasts
Autophagy
Human muscle stem/progenitor cells
Duchenne muscular dystrophy
Gene network analysis
Allele-specific silencing
Human artificial chromosomes
Motor neuron
CMS
CRISPR/Cas9
MT RNA/DNA Editing
Bile acid
Eteplirsen
Mdx
Conjugation
Laminographie
Antisense morpholino
Gut microbiota
Myotube
Lamina-associated domain
Cell biology
Neuromuscular junction
BAF
Cell-penetrating peptide
Developmental biology
CLS
DMD
Coculture
Migration
Glucose
Becker muscular dystrophy
Muscle
Chromatin
Insulin
KLF15
Lamin A/C nuclei
Differentiation
Exondys 51
Immortalisation
Allele-specific silencing therapy
Drisapersen
RNA interference
Becker muscular dystrophy BMD Duchenne muscular dystrophy DMD miRNA nNOS
Skeletal muscle
Gene therapy
Folding-defective proteins